Cystic nephromas, previously known as multilocular cystic nephromas, are rare benign renal neoplasms classically occurring in adult females in the 4 th and 5 th decades. As of the 2016 WHO classification, they are considered distinct from pediatric cystic nephromas which have associated DICER1 gene … See more Evolving terminology regarding cystic nephromasand other cystic renal tumors reflects ongoing changes in classification, in step with shifting understanding of the disease processes and genetic aberrations. … See more Patients usually present with abdominal pain and a palpable abdominal mass 12, however some cases may be asymptomatic and incidentally discovered on imaging. See more Multilocular cystic renal tumors generally have the appearance of a multilocular cystic encapsulated mass on most modalities. May … See more Grossly, multilocular cystic renal tumors are typically unifocal multiloculated cystic masses surrounded by a thick fibrous capsule and … See more
Spectrum of Preneoplastic and Neoplastic Cystic Lesions of the Kidney …
WebJun 26, 2024 · Renal medullary carcinoma (RMC) is a rare renal malignancy that has been associated with sickle hemoglobinopathies. RMC is aggressive, difficult to treat, and occurs primarily in adolescents and young adults of African ancestry. This cancer is driven by the loss of SMARCB1, a tumor suppressor seen in a number of primarily rare childhood … WebAug 12, 2024 · Cystic Nephroma of Kidney: It is an uncommon and benign cystic tumor that may be present in both children and adults. The tumor is usually single and typically affects only one kidney. Diffuse Large B-Cell Lymphoma (DLBCL) of Kidney: It is a rare B-cell non-Hodgkin’s lymphoma that affects older adults. It is a common subtype of … philip j hinton
Cystic nephroma: A multicystic renal neoplasm - ScienceDirect
WebOne case was extensively cystic and had hypocellular areas that simulated cystic nephroma; this neoplasm recurred 3 years later as a solid, highly cellular spindle cell sarcoma in the abdominal cavity. The morphology and immunoprofile of these renal neoplasms was compared with a control group of other sarcomas with BCOR genetic … WebJan 3, 2024 · Cystic renal lesions are a common incidental finding on routinely imaging examinations. Although a benign simple cyst is usually easy to recognize, the same is not true for complex and multifocal cystic renal lesions, whose differential diagnosis includes both neoplastic and non-neoplastic conditions. WebJan 15, 2015 · Cystic renal diseases can be categorized as focal, multifocal, or infectious lesions. Diseases that manifest with focal lesions, such as cystic renal cell carcinoma, mixed epithelial and stromal tumor, and cystic nephroma, are often difficult to differentiate but have differing implications for follow-up after resection. philip j fry height